Case Report
We report a 17-year-old boy with Klippel-Trénaunay syndrome (KTS) who underwent total hip arthroplasty with subtrochanteric shortening osteotomy through an extensile direct anterior approach (DAA) in the setting of Crowe IV hip dysplasia. The patient was transitioned from toe-touch weight-bearing to a progressive weight-bearing protocol at 6 weeks postoperatively and was ambulating painlessly at 3 months./r/nPatients with KTS undergoing orthopaedic surgical intervention necessitate a multidisciplinary approach to care. This case demonstrates that THA in Crowe IV hip dysplasia with an associated subtrochanteric shortening osteotomy can be safely and successfully performed through an extensile DAA in this population.